Clinical Manifestations of Parkinson’s Disease Dementia (PDD)

Clinical Manifestations of Parkinson’s Disease Dementia (PDD)

1. Overview
As early as 1877, Jean-Martin Charcot described cognitive and personality changes in Parkinson’s disease (PD) patients. However, Parkinson’s disease dementia (PDD) gained significant attention only in the 1960s. Studies indicate that ‌24–31% of PD patients develop PDD‌, with ‌70–80% of PD patients eventually progressing to PDD‌. PDD accounts for ‌3–4% of all dementia cases‌, and approximately ‌10% of PD patients transition to PDD annually‌. PDD severely impacts social functioning and quality of life in the elderly.


Clinical Features of PDD

1. Extrapyramidal Symptoms

  • Characteristics‌:
    • Dominated by ‌axial symptoms‌ (e.g., postural instability, gait disturbances).
    • Tremor is less common‌, possibly due to dysfunction in non-dopaminergic pathways.
    • Poor response to ‌levodopa therapy‌, reflecting multisystem neurodegeneration.

2. Cognitive Impairment

PDD manifests as ‌subcortical dementia‌ in early/moderate stages, progressing to ‌mixed subcortical-cortical dementia‌ in advanced stages. Deficits involve:

  1. Attention Deficits‌ (29% of patients):
    • Fluctuating attention, reduced alertness, and impaired focus.
    • Assessment‌:
      • Serial subtraction of 7 from 100 (≥2 errors).
      • Reverse recitation of months (errors or >90 seconds to complete).
  2. Executive Dysfunction‌:
    • Impaired planning, task-switching, and problem-solving.
    • Assessment‌:
      • Verbal fluency‌: <11 animals named in 1 minute.
      • Clock-drawing test‌: Errors in numbering or time indication (e.g., 11:10).
  3. Visuospatial Impairment‌:
    • Difficulty with object recognition, shape discrimination, and figure copying.
    • Assessment‌: Figure-copying tasks in the ‌Mini-Mental State Examination (MMSE)‌.
  4. Memory Loss‌:
    • Retrieval-based deficits‌: Impaired recall despite intact encoding/storage (cues improve performance).
    • Assessment‌:
      • MMSE‌: Failure to recall 3 items (e.g., “ball, flag, tree”) after 3–5 minutes.
      • Montreal Cognitive Assessment (MoCA)‌: Delayed recall score ≤3/5; preserved recognition with cues.

3. Neuropsychiatric Symptoms

  • Common‌: Visual hallucinations, illusions, delusions, depression, apathy, and REM sleep behavior disorder.
  • Note‌: Depression may confound cognitive assessments; treat depression first before reevaluating cognition.

Key Diagnostic Tools

  • MMSE‌: Evaluates attention, memory, and visuospatial skills.
  • MoCA‌: Assesses executive function, delayed recall, and orientation.
  • Neuropsychiatric Inventory (NPI)‌: Screens for hallucinations, depression, and sleep disturbances.

Clinical Pearls

  • Early PDD‌: Subcortical deficits (executive dysfunction, slowed processing).
  • Advanced PDD‌: Mixed cortical-subcortical features (aphasia, agnosia).
  • Treatment‌: Cholinesterase inhibitors (e.g., rivastigmine) for cognitive/behavioral symptoms; address psychosis with cautious use of antipsychotics (e.g., quetiapine).

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